Acute development of transverse spinal cord damage because of Chiari malformation type I complicated by syringomyelia
Abstract
Objective: to present the clinical case of acute manifestation of transverse spinal cord damage syndrome in patient 25 years old suffered from Chiari malformation type I and syringomyelia. Material and methods: we present the clinical case of acute transverse spinal cord damage syndrome in patient 25 years old who was follow up examined during 2 years with stable course of Chiari malformation type I and syringomyelia. The emergent operation including craniovertebral decompression with dura mater plasty using fascia lata was performed. Results: the increase of muscle strength in extremities (with full recovery in upper limbs) as well as regress of coordination disturbances in upper limbs and bowel and bladder functions recovery was observed in neurologi cal status after craniovertebral decompression. The control MRI of craniovertebral region and cervical spine performed in 3 months after operation confirmed the formation of adequate cisterna magna and regress of syringomyelia. Conclusion: the acute development of symptoms because of Chiari malformation type I is very rare and occurs approximately in 1% among patients with such pathology according to literature data. The pathogenesis of acute manifestation of symptoms is still not clearly defined. That is why it is necessary to remember about possibility of such acute diseases manifestation while the observation and follow up is prescribed as treatment strategy for patients with Chiari malformation type I and syringomyelia.
About the Authors
G. Yu. Evzikov
Первый МГМУ им. И.М. Сеченова; Клиника нервных болезней Первого Московского государственного медицинского университета им. И.М. Сеченова
Russian Federation
Russian Federation
M. A. Ivanova
Клиника нервных болезней Первого Московского государственного медицинского университета им. И.М. Сеченова
Russian Federation
Russian Federation
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Review
For citations:
Evzikov G.Yu., Ivanova M.A. Acute development of transverse spinal cord damage because of Chiari malformation type I complicated by syringomyelia. Russian journal of neurosurgery. 2016;(4):85-91. (In Russ.)
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