neurosurgeryНейрохирургияRussian journal of neurosurgery1683-32952587-7569Издательский дом "МедИНК"10.63769/1683-3295-2016-0-2-53-58neurosurgery-288Research ArticleНАБЛЮДЕНИЕ ИЗ ПРАКТИКИFROM PRACTICEСКРЫТЫЙ СИНДРОМ ФИКСИРОВАННОГО СПИННОГО МОЗГА У ДЕТЕЙ (КЛИНИЧЕСКОЕ НАБЛЮДЕНИЕ И ОБЗОР ЛИТЕРАТУРЫ)The Occult tethered spinal cord syndrome in children (the clinical case and literature review)СысоевКирилл ВладимировичSysoevK. V.sysoev.rnsi@mail.ruЖароваЕлена НиколаевнаZharovaE. N.noemail@neicon.ruЗабродскаяЮлия МихайловнаZabrodskayaYu. M.noemail@neicon.ruХачатрянВильям АрамовичKhachatryanV. A.noemail@neicon.ruРоссийский нейрохирургический институт им. проф. А.Л. Поленова - филиал ФГБУ «СЗФМИЦ им. В.А. Алмазова» Минздрава РоссииRussian Federation201605102017025358Copyright © Сысоев К.В., Жарова Е.Н., Забродская Ю.М., Хачатрян В.А., 20172017Сысоев К.В., Жарова Е.Н., Забродская Ю.М., Хачатрян В.А.Sysoev K.V., Zharova E.N., Zabrodskaya Y.M., Khachatryan V.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.therjn.com/jour/article/view/288

Целью исследования явилось определение особенностей диагностики и показаний к хирургическому лечению скрытого СФСМ. Материалы и методы. Клиническое, интроскопическое, нейрофизиологическое, урологическое обследование, интраоперационная диагностика и морфометрия проведены у девочки 9 лет. Результаты. Продемонстрирован регресс клинических и электрофизиологических проявлений заболевания после хирургического лечения. Заключение. При наличии стойких к медикаментозной терапии клинических проявлений СФСМ существуют показания к дефиксирующей операции, даже при отсутствии нейровизуализационных признаков фиксации спинного мозга.

Introduction: The one of the actual pediatric neurosurgery problems remains the optimal strategy selection for treatment of occult tethered cord syndrome (TCS), which presents no neuroimaging signs of spinal cord tethering in spite of clinical manifestation and characteristic of TCS. Objective: to define the specific aspects of the TCS diagnostics and to determine the indications for surgical treatment. Methods: clinical, neurovisualization, neurophysiological, urological examination, intraoperative diagnostics and morphometry in female patient 9 years old with TCS. Results: clinical and electrophysiological improvement after surgical treatment was observed. Conclusions: the presence of clinical manifestations of the TCS resistant to drug therapy is an indication for surgery, even in the absence of neuroimaging signs of the spinal cord tethering.

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The authors declare that there are no conflicts of interest present.